REFERRAL GUIDELINES : WHO TO REFER

Confirmed / suspected:

• Idiopathic pulmonary arterial hypertension
• Connective tissue disease associated PAH
• Chronic thromboembolic pulmonary hypertension
• Portopulmonary hypertension

Other associated PAH: HIV; anorexigens; post-correction right-left shunt; sarcoid; sickle cell disease.

Consider Referral pulmonary hypertension in :

• Hypoxic lung disease (COPD, interstitial lung disease, sleep disordered breathing)
• Cardiac disease (R-L cardiac shunt / Eisenmenger?s)

Treatment of PH in these patient groups is not established and evaluation is not usually undertaken. This is, however, an evolving field and referral for assessment should be considered if symptoms or echo pressures seem excessive (PASP >60mmHg) or there are other PH associated conditions.

Patients with pulmonary hypertension secondary to left heart disease are not currently evaluated, unless there are other PH associated conditions.